ICD-11 classes
09 Diseases of the visual system
Strabismus or ocular motility disorders
Diseases of neuromuscular junction or muscle
Primary disorders of muscles

ICD-11 Primary disorders of muscles

Disorders in which the primary symptom of muscle weakness is secondary to a specific dysfunction of a muscle fiber.

The diagnosis includes nothing.

It excludes 2 items.

  • Metabolic disorders (5C50-5D2Z)
  • Arthrogryposis multiplex congenita (LD26.41)

Diagnosis contains 13 clarifying diagnoses:

  1. 8C70 — Muscular dystrophy
    It contains 10 clarifying diagnoses.
  2. 8C71 — Myotonic disorders
    It contains 8 clarifying diagnoses.
  3. 8C72 — Congenital myopathies
    It contains 4 clarifying diagnoses.
  4. 8C73 — Mitochondrial myopathies
    It contains 6 clarifying diagnoses.
  5. 8C74 — Periodic paralyses or disorders of muscle membrane excitability
    It contains 4 clarifying diagnoses.
  6. 8C75 — Distal myopathies
  7. 8C76 — Myofibrillar myopathy
  8. 8C77 — Ocular myopathy
  9. 8C78 — Malignant hyperthermia or hyperpyrexia
  10. FB32.20 — Idiopathic rhabdomyolysis
  11. 4A41 — Idiopathic inflammatory myopathy
    It contains 5 clarifying diagnoses.
  12. 8C7Y — Other specified primary disorders of muscles
  13. 8C7Z — Primary disorders of muscles, unspecified

The diagnosis is coded elsewhere:

The diagnosis is included in 2 other classes.

  • Idiopathic rhabdomyolysis (FB32.20)
  • Idiopathic inflammatory myopathy (4A41)

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