ICD-11 classes
11 Diseases of the circulatory system
Pulmonary heart disease or diseases of pulmonary circulation
BB01 — Pulmonary hypertension
BB01.0 — Pulmonary arterial hypertension
ICD-11 BB01.0 — Pulmonary arterial hypertension
Pulmonary arterial hypertension is a clinical condition characterised by the presence of pre-capillary pulmonary hypertension in the absence of other causes of pre-capillary pulmonary hypertension, such as due to lung diseases, chronic thromboembolic pulmonary hypertension, or other rare diseases. It includes different forms that share a similar clinical picture and virtually identical pathological changes of the lung microcirculation.
It includes 2 items.
- primary pulmonary hypertension
- Idiopathic pulmonary arterial hypertension
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
- Pulmonary hypertension #13186