ICD-11 classes
11 Diseases of the circulatory system
Diseases of the myocardium or cardiac chambers
BC43 — Cardiomyopathy
BC43.0 — Dilated cardiomyopathy
BC43.00 — Familial-genetic dilated cardiomyopathy

ICD-11 BC43.00 — Familial-genetic dilated cardiomyopathy

Familial-genetic dilated cardiomyopathy is the presence of dilated cardiomyopathy that is present in multiple members of a pedigree, or in the presence of a genetic mutation known to be significantly associated with dilated cardiomyopathy.Additional information: Candidate cytoskeletal and Z disk–encoding genes, most of whom are hypothesized to lead to abnormalities in force transmission, include δ-sarcoglycan, β-sarcoglycan, desmin, lamin A/C, metavinculin, muscle LIM protein, titin, α-actinin-2, nebulette, myopalladin, and ZASP (Z band alternatively spliced PDZ domain protein)

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.