ICD-11 classes
11 Diseases of the circulatory system
Diseases of the myocardium or cardiac chambers
BC43 — Cardiomyopathy
BC43.3 — Endocardial fibroelastosis
ICD-11 BC43.3 — Endocardial fibroelastosis
Endocardial fibroelastosis is the formation of a marked fibro-elastic thickening of the subendocardium in one or both cardiac ventricles. A disorder of fetuses and infants, secondary causes include congenital left-sided obstructive cardiac lesions, metabolic disorders, autoimmune disease (anti-Ro/ anti-La antibodies), and transplacental viral infection such as mumps. Primary endocardial fibroelastosis has been linked to recessive and x-linked inheritance, such as with Barth syndrome.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: