ICD-11 classes
11 Diseases of the circulatory system
Cardiac arrhythmia
BC65 — Cardiac arrhythmia associated with genetic disorder
BC65.2 — Short QT syndrome

ICD-11 BC65.2 — Short QT syndrome

Familial short QT syndrome is a rare cardiac rhythm disorder that associates a short QT interval (QT and QTc 300 ms) on the surface electrocardiogram (ECG) with a high risk of syncope or sudden death due to malignant ventricular arrhythmia.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.