ICD-11 classes
11 Diseases of the circulatory system
Cardiac arrhythmia
BC65 — Cardiac arrhythmia associated with genetic disorder
BC65.5 — Catecholaminergic polymorphic ventricular tachycardia

ICD-11 BC65.5 — Catecholaminergic polymorphic ventricular tachycardia

Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a severe genetic arrhythmogenic disorder of childhood characterised by adrenergically-induced ventricular tachycardia (bidirectional ventricular tachycardia and, less frequently, supraventricular tachycardia and atrial fibrillation) manifesting as syncope and sudden death.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.