ICD-11 classes
11 Diseases of the circulatory system
Diseases of arteries or arterioles
Chronic arterial occlusive disease
BD42 — Raynaud phenomenon

ICD-11 BD42 — Raynaud phenomenon

Raynaud phenomenon describes an exaggerated vascular response to cold temperature or emotional stimuli resulting in episodic digital ischaemia. It is characterised by paroxysmal vasoconstriction producing initially pallor, an essential component for the diagnosis, followed by cyanosis and erythema. Primary Raynaud disease is an isolated innocuous disorder. Secondary Raynaud phenomenon occurs in association with a wide range of different disorders including dysproteinaemias and non-organ-specific systemic autoimmune diseases.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code BD42 contains 3 clarifying diagnoses:

  1. BD42.0 — Primary Raynaud disease
  2. BD42.1 — Secondary Raynaud phenomenon
  3. BD42.Z — Raynaud phenomenon, unspecified

The diagnosis is coded elsewhere:

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