ICD-11 classes
11 Diseases of the circulatory system
Diseases of arteries or arterioles
BD52 — Certain specified disorders of arteries or arterioles
BD52.0 — Segmental arterial mediolysis

ICD-11 BD52.0 — Segmental arterial mediolysis

Segmental arterial mediolysis is a rare noninflammatory vascular disease of the abdominal splanchnic arteries, characterised by disruption of the arterial medial layer. It will induce multiple aneurysms in mesenteric arteries with susceptibility to vessel dissection, haemorrhage and mesenteric ischemia.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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