ICD-11 classes
11 Diseases of the circulatory system
Developmental anomalies of the circulatory system
Structural developmental anomalies of the circulatory system
Structural developmental anomaly of heart or great vessels

ICD-11 Structural developmental anomaly of heart or great vessels

A congenital malformation of the heart and/or great vessels or an acquired abnormality unique to the congenitally malformed heart.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis contains 20 clarifying diagnoses:

1. LA80 — Anomalous position-orientation of heart
   It contains 6 clarifying diagnoses.
2. LA81 — Abnormal ventricular relationships
3. LA82 — Total mirror imagery
4. LA83 — Right isomerism
5. LA84 — Left isomerism
6. LA85 — Congenital anomaly of an atrioventricular or ventriculo-arterial connection
   It contains 7 clarifying diagnoses.
7. LA86 — Congenital anomaly of mediastinal vein
   It contains 6 clarifying diagnoses.
8. LA87 — Congenital anomaly of an atrioventricular valve or atrioventricular septum
   It contains 6 clarifying diagnoses.
9. LA88 — Congenital anomaly of a ventricle or the ventricular septum
   It contains 7 clarifying diagnoses.
10. LA89 — Functionally univentricular heart
    It contains 6 clarifying diagnoses.
11. LA8A — Congenital anomaly of a ventriculo-arterial valve or adjacent regions
    It contains 9 clarifying diagnoses.
12. LA8B — Congenital anomaly of great arteries including arterial duct
    It contains 7 clarifying diagnoses.
13. LA8C — Congenital anomaly of coronary artery
    It contains 5 clarifying diagnoses.
14. LA8D — Congenital pericardial anomaly
15. LA8E — Congenital anomaly of atrial septum
    It contains 6 clarifying diagnoses.
16. LA8F — Congenital anomaly of right atrium
17. LA8G — Congenital anomaly of left atrium
    It contains 3 clarifying diagnoses.
18. BD52.6 — Congenital great vessel related acquired abnormality
    It contains 2 clarifying diagnoses.
19. LA8Y — Other specified structural developmental anomaly of heart or great vessels
20. LA8Z — Structural developmental anomaly of heart or great vessels, unspecified

The diagnosis is coded elsewhere:

• Structural developmental anomalies of the circulatory system #22515
• Structural developmental anomaly of heart or great vessels #22516