ICD-11 classes
11 Diseases of the circulatory system
Cerebrovascular diseases
8B22 — Certain specified cerebrovascular diseases
8B22.B — Moyamoya syndrome
ICD-11 8B22.B — Moyamoya syndrome
A cerebrovascular disease caused by stenotic arteries at the base of the brain in the basal ganglia. Moyamoya, meaning «puff of smoke» refers to the appearance of the anastomotic vessel network formed at the base of the brain distal to the circle of Willis to compensate for the blockage.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: