ICD-11 classes
11 Diseases of the circulatory system
Cerebrovascular diseases
8B22 — Certain specified cerebrovascular diseases
8B22.C — Hereditary cerebrovascular diseases

ICD-11 8B22.C — Hereditary cerebrovascular diseases

Hereditary cerebrovascular disease does not include effects from abnormalities due other vascular diseases which are independent of the nervous system.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 8B22.C contains 4 clarifying diagnoses:

  1. 8B22.C0 — CADASIL - [cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy] syndrome
  2. 8B22.C1 — CARASIL - [cerebral autosomal recessive arteriopathy with subcortical infarcts and leukoencephalopathy] syndrome
  3. 8B22.CY — Other specified hereditary cerebrovascular diseases
  4. 8B22.CZ — Hereditary cerebrovascular diseases, unspecified

The diagnosis is coded elsewhere:

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