ICD-11 classes
12 Diseases of the respiratory system
Respiratory diseases principally affecting the lung...
CB03 — Idiopathic interstitial pneumonitis
CB03.4 — Idiopathic pulmonary fibrosis

ICD-11 CB03.4 — Idiopathic pulmonary fibrosis

Idiopathic pulmonary fibrosis (IPF) is defined as a specific form of chronic, progressive fibrosing interstitial pneumonia (pneumonitis) of unknown cause, occurring primarily in older adults, limited to the lungs, and associated with the histopathologic and/or radiologic pattern of UIP. The definition of IPF requires the exclusion of other forms of interstitial pneumonia (pneumonitis) including other idiopathic interstitial pneumonias (pneumonitis) and Interstitial Lung Disease (ILD) associated with environmental exposure, medication, or systemic disease.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.