ICD-11 classes
12 Diseases of the respiratory system
Respiratory diseases principally affecting the lung...
CB04 — Primary interstitial lung diseases specific to infancy or...
CB04.2 — Disorders of surfactant metabolism

ICD-11 CB04.2 — Disorders of surfactant metabolism

Primary interstitial lung disease specific to childhood due to pulmonary surfactant protein anomalies is a group of interstitial lung diseases (ILD) induced by genetic mutations disrupting surfactant function and gas exchange in the lung. The disorders caused by these mutations affect full-term infants and older children and exhibit considerable overlap in their clinical and histologic presentation

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.