ICD-11 classes
12 Diseases of the respiratory system
Respiratory diseases principally affecting the lung...
CB04 — Primary interstitial lung diseases specific to infancy or...
CB04.3 — Alveolar or peri-alveolar conditions
CB04.31 — Pulmonary alveolar proteinosis

ICD-11 CB04.31 — Pulmonary alveolar proteinosis

This is a rare lung disease in which abnormal accumulation of surfactant occurs within the alveoli, interfering with gas exchange. PAP can occur in a primary form or secondarily in the settings of malignancy (especially in myeloid leukemia), pulmonary infection, or environmental exposure to dusts or chemicals.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.