ICD-11 classes
12 Diseases of the respiratory system
Respiratory diseases principally affecting the lung...
CB04 — Primary interstitial lung diseases specific to infancy or...
CB04.4 — Pulmonary capillaritis

ICD-11 CB04.4 — Pulmonary capillaritis

Isolated pauciimmune pulmonary capillaritis is a small vessel vasculitis restricted to the lungs that may induce diffuse alveolar haemorrhage with dyspnoea, anaemia, chest pain, haemoptysis, bilateral and diffuse alveolar infiltrates at chest X-rays, without any underlying systemic disease. ANCA are frequently positive but could be negative.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.