ICD-11 classes
12 Diseases of the respiratory system
Respiratory diseases principally affecting the lung...
CB05 — Interstitial lung diseases associated with systemic diseases
CB05.4 — Interstitial lung diseases associated with systemic...
CB05.41 — Respiratory disorders in microscopic polyangiitis

ICD-11 CB05.41 — Respiratory disorders in microscopic polyangiitis

This encompasses pathological conditions affecting the organs and tissues that make gas exchange possible in higher organisms, and includes conditions of the upper respiratory tract, trachea, bronchi, bronchioles, alveoli, pleura and pleural cavity, and the nerves and muscles of breathing. This diagnosis is in an ill-defined autoimmune disease characterised by a systemic, pauci-immune, necrotizing, small-vessel vasculitis without clinical or pathological evidence of necrotizing granulomatous inflammation.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.