ICD-11 classes
12 Diseases of the respiratory system
Respiratory diseases principally affecting the lung...
CB07 — Lymphangioleiomyomatosis

ICD-11 CB07 — Lymphangioleiomyomatosis

Lymphangioleiomyomatosis (LAM) is a multiple cystic lung disease characterised by progressive cystic destruction of the lung and lymphatic abnormalities, frequently associated with renal angiomyolipomas (AMLs). LAM occurs either sporadically or as a manifestation of tuberous sclerosis complex (TSC, ).

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code CB07 contains 4 clarifying diagnoses:

1. CB07.0 — Lymphangioleiomyomatosis associated with tuberous sclerosis complex
2. CB07.1 — Sporadic lymphangioleiomyomatosis
3. CB07.Y — Other specified lymphangioleiomyomatosis
4. CB07.Z — Lymphangioleiomyomatosis, unspecified