ICD-11 classes
12 Diseases of the respiratory system
Pulmonary heart disease or diseases of pulmonary circulation
BB01 — Pulmonary hypertension
BB01.3 — Chronic thromboembolic pulmonary hypertension
ICD-11 BB01.3 — Chronic thromboembolic pulmonary hypertension
Chronic thromboembolic pulmonary hypertension (CTEPH) is characterised by the persistence of thromboemboli in the form of organised tissue obstructing the pulmonary arteries. The consequence is an increase in pulmonary vascular resistance (PVR) resulting in pulmonary hypertension (PH) and progressive right heart failure.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
- Chronic pulmonary thromboembolism #11013
- Pulmonary hypertension #11016
- Chronic pulmonary thromboembolism #13183