ICD-11 classes
13 Diseases of the digestive system
Diseases of small intestine
DA90 — Nonstructural developmental anomalies of small intestine
DA90.1 — Congenital intestinal transport defect
ICD-11 DA90.1 — Congenital intestinal transport defect
This is a congenital disease of the small intestinal mucosa that presents with intractable diarrhoea and malabsorption of nutrients in young children, due to defect of transporter of nutrients in enterocytes.
The diagnosis includes nothing.
The diagnosis excludes nothing.
Diagnosis with code DA90.1 contains 3 clarifying diagnoses:
- 5C61.0 — Glucose-galactose malabsorption
- 5C61.40 — Fructose malabsorption
- 5C64.20 — Acrodermatitis enteropathica
The diagnosis is included in 10 other classes.
- Glucose-galactose malabsorption (5C61.0)
- Fructose malabsorption (5C61.40)
- Acrodermatitis enteropathica (5C64.20)
- Idiopathic bile acid malabsorption (DA96.02)
- Hereditary megaloblastic anaemia due to transcobalamin deficiency (3A01.0)
- Glycogen storage disease due to GLUT2 deficiency (5C51.3)
- Lysinuric protein intolerance (5C60.Y)
- Haptocorrin deficiency (5C63.0)
- Hereditary folate malabsorption (5C63.1)
- Vitamin B12 deficiency anaemia due to selective vitamin B12 malabsorption with proteinuria (3A01.Y)