ICD-11 classes
13 Diseases of the digestive system
Diseases of liver
DB98 — Vascular disorders of the liver
LA90.00 — Hereditary haemorrhagic telangiectasia
ICD-11 LA90.00 — Hereditary haemorrhagic telangiectasia
Rendu-Osler-Weber disease, also called hereditary haemorrhagic telangiectasia (HHT), is a genetic disorder of angiogenesis leading to arteriovenous dilatations: cutaneo-mucosal haemorrhagic telangiectasias and visceral shunting.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
- Capillary malformations #12161
- Genetic or developmental disorders involving lips or oral mucosa #13302
- Angiodysplasia of stomach #13654
- Angiodysplasia of small intestine #13947
- Genetic or developmental disorders involving lips or oral mucosa #15229
- Genetic syndromes affecting cutaneous vasculature #15939
- Genetic syndromes affecting cutaneous vasculature #16583
- Genetic or developmental disorders involving lips or oral mucosa #16873
- Capillary malformations #22695
- Genetic or developmental disorders involving lips or oral mucosa #22812