ICD-11 classes
01 Certain infectious or parasitic diseases
Human prion diseases
8E01 — Acquired prion disease

ICD-11 8E01 — Acquired prion disease

Environmentally acquired prion diseases are prion diseases caused by a known source of abnormal prion protein.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 8E01 contains 4 clarifying diagnoses:

1. 8E01.0 — Iatrogenically acquired Creutzfeldt-Jakob Disease
2. 8E01.1 — Kuru
3. 8E01.2 — Variant Creutzfeldt-Jakob Disease
4. 8E01.3 — Other acquired Creutzfeldt-Jakob Disease

The diagnosis is coded elsewhere:

• Human prion diseases #7722