ICD-11 classes
14 Diseases of the skin
Inflammatory dermatoses
Papulosquamous dermatoses
EA94 — Pityriasis rubra pilaris

ICD-11 EA94 — Pityriasis rubra pilaris

Pityriasis rubra pilaris (PRP) is the name given to a group of clinically similar papulosquamous dermatoses of unknown aetiology. They initially present with erythematous, hyperkeratotic perifollicular papules, which tend to coalesce into plaques, but may progress to erythroderma, particularly in adults. The distribution, age of onset and speed of onset differ markedly between patients and these differences have been used to classify PRP into a number of clinically distinct subtypes.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.