ICD-11 classes
14 Diseases of the skin
Inflammatory dermatoses
Immunobullous diseases of the skin

ICD-11 Immunobullous diseases of the skin

A group of disorders characterised by the presence of circulating auto-antibodies directed against specific skin or mucous membrane antigens and resulting in blisters or erosions.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis contains 6 clarifying diagnoses:

  1. EB40 — Pemphigus
    It contains 6 clarifying diagnoses.
  2. EB41 — Pemphigoid
    It contains 4 clarifying diagnoses.
  3. EB42 — Linear IgA bullous dermatosis
  4. EB43 — Epidermolysis bullosa acquisita
  5. EB44 — Dermatitis herpetiformis
  6. EB4Y — Other specified immunobullous disorder

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