ICD-11 classes
14 Diseases of the skin
Inflammatory dermatoses
Nonorgan specific systemic autoimmune disorders involving...

ICD-11 Nonorgan specific systemic autoimmune disorders involving the skin

This group incorporates a number of complex auto-immune disorders which are characterised by their ability to affect multiple organ systems including the skin. Examples include systemic lupus erythematosus and dermatomyositis.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis contains 6 clarifying diagnoses:

  1. 4A40.00 — Systemic lupus erythematosus with skin involvement
  2. 4A41.0 — Dermatomyositis
    It contains 3 clarifying diagnoses.
  3. 4A42 — Systemic sclerosis
    It contains 4 clarifying diagnoses.
  4. 4A45 — Antiphospholipid syndrome
    It contains 5 clarifying diagnoses.
  5. 4A43 — Overlap or undifferentiated nonorgan specific systemic autoimmune disease
    It contains 7 clarifying diagnoses.
  6. FB82.3 — Relapsing polychondritis

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