ICD-11 classes
14 Diseases of the skin
Metabolic and nutritional disorders affecting the skin
EB90 — Dermatoses resulting from disturbed metabolic processes
EB90.3 — Porphyria or pseudoporphyria affecting the skin
5C58.13 — Variegate porphyria
ICD-11 5C58.13 — Variegate porphyria
Variegate porphyria is a form of acute hepatic porphyria characterised by the occurrence of neuro-visceral attacks with or without the presence of cutaneous lesions (bullous photodermatitis).
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
- Porphyrias #4925
- Liver diseases due to disorders of porphyrin or bilirubin metabolism or transport #5089
- Liver diseases due to disorders of porphyrin or bilirubin metabolism or transport #14406
- Genetic and developmental disorders affecting the skin #15936
- Porphyria or pseudoporphyria affecting the skin #17243