ICD-11 classes
14 Diseases of the skin
Genetic and developmental disorders affecting the skin
Genetic syndromes affecting the skin
LD27.0 — Ectodermal dysplasia syndromes
LD27.01 — Cronkhite-Canada syndrome
ICD-11 LD27.01 — Cronkhite-Canada syndrome
Cronkhite-Canada syndrome (CCS) is a sporadically occurring, noninherited disorder of generalised gastrointestinal polyps (hamartomas), cutaneous pigmentation, alopecia, and onychodystrophy. The possibility of progression to cancer is considered to be low. Chronic diarrhea and protein-losing enteropathy are often observed.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
- Polyposis syndrome #2669
- Polyposis syndrome #14141
- Polyposis syndrome #14174
- Ectodermal dysplasia syndromes #23325