ICD-11 classes
14 Diseases of the skin
Genetic and developmental disorders affecting the skin
EC22 — Genetic defects of nails or nail growth
LD27.4 — Genetic syndromes affecting nails
LD27.03 — Hidrotic ectodermal dysplasia, Clouston type
ICD-11 LD27.03 — Hidrotic ectodermal dysplasia, Clouston type
Clouston syndrome (or hidrotic ectodermal dysplasia) is an inherited disorder characterised by the clinical triad of nail dystrophy, alopecia, and palmoplantar hyperkeratosis.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
- Ectodermal dysplasia syndromes #15941
- Diffuse palmoplantar keratodermas #15961
- Genetic syndromes with alopecia or hypotrichosis #15975
- Diffuse palmoplantar keratodermas #16235
- Genetic syndromes with alopecia or hypotrichosis #16341
- Genetic syndromes affecting nails #16460
- Ectodermal dysplasia syndromes #23325
- Genetic syndromes affecting nails #23337