ICD-11 classes
14 Diseases of the skin
Genetic and developmental disorders affecting the skin
Genetic disorders affecting dermal collagen, elastin or...
EC40 — Pseudoxanthoma elasticum
ICD-11 EC40 — Pseudoxanthoma elasticum
Pseudoxanthoma elasticum (PXE) is an inherited connective tissue disorder characterised by progressive calcification and fragmentation of elastic fibres in the skin, retina, and arterial walls.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: