ICD-11 classes
14 Diseases of the skin
Genetic and developmental disorders affecting the skin
Specified developmental anomalies affecting the skin
LA31 — Structural developmental anomalies of mouth or tongue
LA31.3 — Macrostomia

ICD-11 LA31.3 — Macrostomia

Congenital macrostomia or transverse facial cleft is a rare congenital craniofacial anomaly. It is usually associated with deformities of other structures developed from the first and second branchial arches and is thought to be part of the manifestations of hemifacial microsomia, the second most common congenital craniofacial anomaly.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

• Structural developmental anomalies of mouth or tongue #13473
• Structural developmental anomalies of mouth or tongue #22431