ICD-11 classes
14 Diseases of the skin
Genetic and developmental disorders affecting the skin
4A60 — Monogenic autoinflammatory syndromes
ICD-11 4A60 — Monogenic autoinflammatory syndromes
Monogenic hereditary autoinflammatory diseases characterised by apparently unprovoked generalised inflammation in the absence of infection or high titre autoantibodies.
The diagnosis includes nothing.
The diagnosis excludes nothing.
Diagnosis with code 4A60 contains 5 clarifying diagnoses:
- 4A60.0 — Familial Mediterranean fever
- 4A60.1 — Cryopyrin-associated periodic syndromes
- 4A60.2 — Tumour necrosis factor receptor 1 associated periodic syndrome
- 4A60.Y — Other specified monogenic autoinflammatory syndromes
- 4A60.Z — Autoimflammatory syndrome, unspecified
The diagnosis is coded elsewhere: