ICD-11 classes
14 Diseases of the skin
Sensory and psychological disorders affecting the skin
Neurological conditions affecting the skin
8C21 — Hereditary sensory or autonomic neuropathy
8C21.2 — Hereditary sensory and autonomic neuropathy type IV
ICD-11 8C21.2 — Hereditary sensory and autonomic neuropathy type IV
Hereditary sensory and autonomic neuropathy, type 4 (HSAN4) is an inherited disorder characterised by anhidrosis, insensitivity to pain, self-mutilating behaviour and episodes of fever.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
- Hereditary sensory or autonomic neuropathy #7360
- Hereditary sensory or autonomic neuropathy #7669
- Hypohidrosis attributable to defective sudomotor innervation or function #7712
- Hypohidrosis due to genetic abnormalities of eccrine gland structure or function #7714
- Hypohidrosis attributable to defective sudomotor innervation or function #16411
- Hypohidrosis due to genetic abnormalities of eccrine gland structure or function #16413
- Conditions with disorders of intellectual development as a relevant clinical feature #23735