ICD-11 classes
14 Diseases of the skin
Skin disorders involving specific cutaneous structures
Disorders of the epidermis and epidermal appendages
Disorders of epidermal keratinisation

ICD-11 Disorders of epidermal keratinisation

This group incorporates dermatoses characterised by scaling (ichthyoses and hyperkeratoses), epidermal thickening (acanthoses and keratodermas), loss of cohesion (acantholytic dermatoses and skin peeling) or xeroderma.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis contains 9 clarifying diagnoses:

  1. ED50 — Ichthyoses
    It contains 4 clarifying diagnoses.
  2. ED51 — Diffuse epidermal hyperkeratosis and acanthosis
    It contains 2 clarifying diagnoses.
  3. ED52 — Porokeratoses
  4. ED53 — Skin peeling
    It contains 1 clarifying diagnosis.
  5. ED54 — Xerosis cutis or asteatosis
    It contains 1 clarifying diagnosis.
  6. ED55 — Palmoplantar keratodermas
    It contains 3 clarifying diagnoses.
  7. ED56 — Keratosis pilaris
  8. EC20.2 — Hereditary acantholytic dermatoses
  9. ED5Y — Other specified disorders of epidermal keratinisation

The diagnosis is included in 1 another class.

  • Hereditary acantholytic dermatoses (EC20.2)

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