ICD-11 classes
14 Diseases of the skin
Skin disorders involving specific cutaneous structures
Disorders of the dermis and subcutis
Disorders of subcutaneous fat
EF01 — Lipoatrophy or lipodystrophy
LD27.6 — Genetic lipodystrophy
ICD-11 LD27.6 — Genetic lipodystrophy
Genetic lipodystrophies represent a heterogeneous group of rare diseases characterised by a generalised or localised loss of body fat (lipoatrophy).
The diagnosis includes nothing.
The diagnosis excludes nothing.
Diagnosis with code LD27.6 contains 2 clarifying diagnoses:
- LD27.60 — Congenital generalised lipodystrophy
- LD27.6Z — Genetic lipodystrophy, unspecified
The diagnosis is coded elsewhere:
- Genetic disorders of adipose tissue or lipid metabolism affecting the skin #16063
- Genetic lipodystrophy #16067
- Syndromes with skin or mucosal anomalies as a major feature #23324
- Genetic lipodystrophy #23351
The diagnosis is included in 2 other classes.
- Familial partial lipodystrophy (5A44)
- Wiedemann-Rautenstrauch progeroid syndrome (LD2B)