ICD-11 classes
14 Diseases of the skin
Skin disorders involving specific cutaneous structures
Disorders of the dermis and subcutis
2A21.1 — Cutaneous mastocytosis
ICD-11 2A21.1 — Cutaneous mastocytosis
Cutaneous mastocytosis is characterised by abnormal accumulation and proliferation of cutaneous mast cells. Most types are isolated but cutaneous mastocytosis can occur in association with systemic disease. Clinical forms include cutaneous mastocytoma, urticaria pigmentosa (the most frequent form), pseudoxanthomatous nodular cutaneous mastocytosis, telangiectasia macularis eruptiva perstans and diffuse cutaneous mastocytosis.
The diagnosis includes nothing.
The diagnosis excludes nothing.
Diagnosis with code 2A21.1 contains 2 clarifying diagnoses:
- 2A21.10 — Urticaria pigmentosa
- 2A21.1Y — Other specified cutaneous mastocytosis
The diagnosis is coded elsewhere:
- Mastocytosis #1555
- Cutaneous mastocytosis #1560
- Mastocytosis #3206
- Cutaneous mastocytosis #3211