ICD-11 classes
14 Diseases of the skin
Skin disorders involving specific cutaneous structures
Disorders of cutaneous blood and lymphatic vessels
Malformations involving cutaneous blood vessels
Developmental anomalies of cutaneous vasculature
LC50 — Developmental capillary vascular malformations of the skin
LC50.1 — Port-wine stain

ICD-11 LC50.1 — Port-wine stain

A port-wine stain is defined as a macular telangiectatic area of skin which is present at birth and does not spontaneously involute. Port-wine stains may be localised or extensive and they are often associated with an underlying disorder.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

• Developmental capillary vascular malformations of the skin #12163
• Developmental capillary vascular malformations of the skin #16126
• Developmental capillary vascular malformations of the skin #22697
• Developmental capillary vascular malformations of the skin #23180