ICD-11 classes
14 Diseases of the skin
Skin disorders involving specific cutaneous structures
Disorders of cutaneous blood and lymphatic vessels
EF40 — Vasculitis or capillaritis involving the skin

ICD-11 EF40 — Vasculitis or capillaritis involving the skin

A range of conditions characterised by inflammation of cutaneous blood vessels with or without extravasation of red blood cells into the interstitium.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code EF40 contains 9 clarifying diagnoses:

  1. EF40.0 — Capillaritis
  2. EF40.1 — Vasculitis affecting small cutaneous blood vessels
    It contains 7 clarifying diagnoses.
  3. EF40.2 — Localised cutaneous vasculitis
    It contains 2 clarifying diagnoses.
  4. 4A44.2 — Giant cell arteritis
  5. 4A44.5 — Mucocutaneous lymph node syndrome
  6. 4A44.6 — Sneddon syndrome
  7. 4A44.8 — Thromboangiitis obliterans
  8. EA93 — Pityriasis lichenoides
  9. EF40.Z — Cutaneous vasculitis unspecified

The diagnosis is included in 6 other classes.

  • Giant cell arteritis (4A44.2)
  • Mucocutaneous lymph node syndrome (4A44.5)
  • Sneddon syndrome (4A44.6)
  • Thromboangiitis obliterans (4A44.8)
  • Pityriasis lichenoides (EA93)
  • Vasculitis associated with probable aetiology (4A44.Y)

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