ICD-11 classes
14 Diseases of the skin
Skin disorders involving specific cutaneous structures
Disorders of cutaneous blood and lymphatic vessels
Malformations involving cutaneous lymphatic vessels
LA90.1 — Lymphatic malformations

ICD-11 LA90.1 — Lymphatic malformations

Lymphatic malformations (LM), formerly referred to by the term lymphangioma, are malformations of the lymphatic system which result in obstructed lymphatic drainage. There are two types of LM: macrocystic LM (including cystic hygroma/lymphangioma) and tissue-infiltrating microcystic LM (lymphangioma circumscriptum). The macro and microcystic forms of LM may occur in association.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code LA90.1 contains 7 clarifying diagnoses:

1. LA90.10 — Macrocystic lymphatic malformation
2. LA90.11 — Microcystic lymphatic malformation
3. LA90.12 — Lymphatic malformations of certain specified sites
4. LA90.13 — Cystic hygroma in fetus
5. BD93.0 — Primary lymphoedema
   It contains 2 clarifying diagnoses.
6. LA90.1Y — Other specified lymphatic malformations
7. LA90.1Z — Lymphatic malformations, unspecified

The diagnosis is coded elsewhere:

• Disorders of lymphatic vessels or lymph nodes #11623
• Lymphatic malformations #11659
• Structural developmental anomalies of the peripheral vascular system #12160
• Lymphatic malformations #12169
• Structural developmental anomalies of the peripheral vascular system #22694
• Lymphatic malformations #22703