ICD-11 classes
14 Diseases of the skin
Adverse cutaneous reactions to medication
Drug eruptions
EH65 — DRESS syndrome

ICD-11 EH65 — DRESS syndrome

DRESS syndrome (Drug Rash with Eosinophilia and Systemic Symptoms) is a hypersensitivity reaction characterised by a generalised skin rash, fever, eosinophilia, lymphocytosis and visceral involvement (hepatitis, nephritis, pneumonitis, pericarditis and myocarditis) and, in some patients, reactivation of human herpes virus 6.

It includes 1 item.

  • Drug-induced hypersensitivity syndrome

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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