ICD-11 classes
14 Diseases of the skin
Skin disorders provoked by external factors
Dermatoses provoked by light or UV radiation
EB90.3 — Porphyria or pseudoporphyria affecting the skin
5C58.10 — Porphyria cutanea tarda
ICD-11 5C58.10 — Porphyria cutanea tarda
Porphyria cutanea tarda (PCT) is due to an accumulation of uroporphyrins in plasma from blockage of the normal haem synthetic pathway in the liver at the level of uroporphyrinogen decarboxylase (URO-D). The majority of cases are sporadic and frequently associated with iron overload. PCT manifests as skin fragility and blistering in light-exposed skin, particularly on the dorsa of the hands, together with hypertrichosis.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: