ICD-11 classes
02 Neoplasms
Neoplasms of haematopoietic or lymphoid tissues
2B31 — Histiocytic or dendritic cell neoplasms
2B31.2 — Langerhans cell histiocytosis
ICD-11 2B31.2 — Langerhans cell histiocytosis
A neoplastic proliferation of Langerhans cells which contain Birbeck granules by ultrastructural examination. Three major overlapping syndromes are recognised: eosinophilic granuloma, Letterer-Siwe disease, and Hand-Schuller-Christian disease. The clinical course is generally related to the number of organs affected at presentation.
It includes 1 item.
- Histiocytosis X
The diagnosis excludes nothing.
Diagnosis with code 2B31.2 contains 2 clarifying diagnoses:
- 2B31.20 — Langerhans cell histiocytosis involving the skin
- 2B31.2Y — Other specified Langerhans cell histiocytosis
The diagnosis is coded elsewhere: