ICD-11 classes
02 Neoplasms
Neoplasms of haematopoietic or lymphoid tissues
2B31 — Histiocytic or dendritic cell neoplasms
2B31.3 — Langerhans cell sarcoma
ICD-11 2B31.3 — Langerhans cell sarcoma
A neoplastic proliferation of Langerhans cells with overtly malignant cytologic features. It can be considered a higher grade variant of Langerhans cell histiocytosis (LCH) and it can present de novo or progress from antecedent LCH.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: