ICD-11 classes
14 Diseases of the skin
Malignant neoplasms involving the skin
Cutaneous lymphoma
Primary cutaneous B-cell lymphomas

ICD-11 Primary cutaneous B-cell lymphomas

Primary cutaneous B-cell lymphomas (CBCL) are malignant lymphoproliferative diseases of unknown cause that are thought to originate from B-lymphocytes in the lymphoid tissue of the skin and by definition are confined to the skin at initial diagnosis.

The diagnosis includes nothing.

Diagnosis contains 3 clarifying diagnoses:

1. 2A80.3 — Primary cutaneous follicle centre lymphoma
2. 2A81.A — Primary cutaneous diffuse large B-cell lymphoma, leg type
3. 2A85.2 — Extranodal marginal zone B-cell lymphoma, primary site skin