ICD-11 classes
14 Diseases of the skin
Malignant neoplasms involving the skin
Cutaneous lymphoma
Mature T-cell or NK-cell lymphomas and lymphoproliferative...
ICD-11 Mature T-cell or NK-cell lymphomas and lymphoproliferative disorders, primary cutaneous specified types
Primary cutaneous T-cell lymphomas (CTCL) and NK-cell lymphomas are malignant lymphoproliferative diseases of unknown cause that are thought to originate from T-lymphocytes in the lymphoid tissue of the skin and by definition are confined to the skin at initial diagnosis. Included in the class is also a small number of lymphoma-like primary cutaneous lymphoproliferative disorders which are not considered to be truly malignant.
It includes 1 item.
- Primary cutaneous peripheral T-cell lymphoma
It excludes 1 item.
- Skin infiltration by nodal or non-cutaneous extranodal lymphoma (2E08)
Diagnosis contains 6 clarifying diagnoses:
- 2B00 — Subcutaneous panniculitis-like T-cell lymphoma
- 2B01 — Mycosis fungoides
- 2B02 — Sézary syndrome
- 2B03 — Primary cutaneous CD-30 positive T-cell lymphoproliferative disorders
It contains 2 clarifying diagnoses. - 2B0Y — Other specified primary cutaneous mature T-cell or NK-cell lymphomas and lymphoproliferative disorders
- 2B0Z — Primary cutaneous T-cell lymphoma of undetermined or unspecified type
The diagnosis is coded elsewhere:
- Mature T-cell or NK-cell neoplasms #1704
- Mature T-cell or NK-cell lymphomas and lymphoproliferative disorders, primary cutaneous specified types #1719
- Mature T-cell or NK-cell neoplasms #3355
- Mature T-cell or NK-cell lymphomas and lymphoproliferative disorders, primary cutaneous specified types #3370