ICD-11 classes
15 Diseases of the musculoskeletal system or connective...
Soft tissue disorders
Disorders of muscles
FB31 — Calcification or ossification of muscle
FB31.1 — Fibrodysplasia ossificans progressiva

ICD-11 FB31.1 — Fibrodysplasia ossificans progressiva

This is an extremely rare disease of the connective tissue where a mutation of the body's repair mechanism causes fibrous tissue (including muscle, tendon, and ligament) to be ossified when damaged.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

• Progressive ossification of skin, skeletal muscle, fascia, tendons or ligaments #18784
• Syndromes with skeletal anomalies as a major feature #18735
• Progressive ossification of skin, skeletal muscle, fascia, tendons or ligaments #23275
• Syndromes with skeletal anomalies as a major feature #23226