ICD-11 classes
15 Diseases of the musculoskeletal system or connective...
Soft tissue disorders
Miscellaneous specified soft tissue disorders
FB51 — Fibroblastic disorders
FB51.4 — Retroperitoneal fibrosis
ICD-11 FB51.4 — Retroperitoneal fibrosis
Retroperitoneal fibrosis (RPF) is a disease characterised by the development of extensive proliferation of fibrous tissue in the retroperitoneum, resulting in entrapment and obstruction of retroperitoneal structures, notably the ureters. RPF can be classified as primary (idiopathic) meaning that the cause is not known or secondary. But its association with various immune-related conditions and response to immunosuppression have led to speculation regarding an autoimmune aetiology of idiopathic RPF. One-third of the cases are secondary to malignancy, medication, trauma, or certain infections.
The diagnosis includes nothing.
The diagnosis excludes nothing.
Diagnosis with code FB51.4 contains 2 clarifying diagnoses:
- FB51.40 — Primary retroperitoneal fibrosis
- FB51.4Y — Other specified retroperitoneal fibrosis