ICD-11 classes
02 Neoplasms
Malignant neoplasms, except primary neoplasms of lymphoid,...
Malignant neoplasms, stated or presumed to be primary, of...
Malignant mesenchymal neoplasms
2B52 — Ewing sarcoma, primary site
2B52.3 — Ewing sarcoma of soft tissue
ICD-11 2B52.3 — Ewing sarcoma of soft tissue
A rare malignant neoplasm of the soft tissues. It is typically a disease of children and young adults. It is characterised by t(11:22) (q24: q12) resulting in the expression of EWS/FLI-1 chimeric transcript. Most commonly occurs in the paravertebral region, chest wall, pelvis and lower extremities.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
- Ewing sarcoma, primary site #11871
- Ewing sarcoma, primary site #18248