ICD-11 classes
15 Diseases of the musculoskeletal system or connective...
Nonorgan specific systemic autoimmune disorders
4A42 — Systemic sclerosis
4A42.1 — Diffuse systemic sclerosis

ICD-11 4A42.1 — Diffuse systemic sclerosis

Diffuse cutaneous systemic sclerosis (dcSSc) is a subtype of Systemic Sclerosis (SSc) characterised by truncal and acral skin fibrosis with an early and significant incidence of diffuse involvement (interstitial lung disease, oliguric renal failure, diffuse gastrointestinal disease, and myocardial involvement).

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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