ICD-11 classes
15 Diseases of the musculoskeletal system or connective...
Nonorgan specific systemic autoimmune disorders
4A43 — Overlap or undifferentiated nonorgan specific systemic...
4A43.1 — Mikulicz disease
ICD-11 4A43.1 — Mikulicz disease
Mikulicz disease is a disorder first reported by Johann von Mikulicz in 1892 and characterised by symmetrical swelling of the lachrymal, submandibular, and parotid glands, with massive infiltration of these glands by mononuclear cells. Serum autoantibodies, such as anti-Ro/SS-A, are usually negative and serum IgG4 concentration may be increased. Unlike Sjögren disease, IgG4-Mikulicz disease is characterised by the formation of lymphoid follicles, but shows lower levels of lymphocytic infiltration into salivary ducts, such that their structure remains intact.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: