ICD-11 classes
15 Diseases of the musculoskeletal system or connective...
Nonorgan specific systemic autoimmune disorders
4A44 — Vasculitis
4A44.9 — Immune complex small vessel vasculitis
4A44.92 — IgA vasculitis

ICD-11 4A44.92 — IgA vasculitis

Vasculitis, with IgA1-dominant immune deposits, affecting small vessels (predominantly capillaries, venules, or arterioles). Often involves skin and gut, and frequently causes arthritis. Glomerulonephritis indistinguishable from IgA nephropathy may occur.

It includes 1 item.

  • Henoch-Schönlein purpura

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

The diagnosis is included in 2 other classes.

  • Respiratory disorders in IgA vasculitis (CB05.4Y)
  • Noninfectious enteritis or ulcer due to IgA vasculitis (DA94.Y)

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