ICD-11 classes
15 Diseases of the musculoskeletal system or connective...
LD24 — Syndromes with skeletal anomalies as a major feature
FB31.1 — Fibrodysplasia ossificans progressiva

ICD-11 FB31.1 — Fibrodysplasia ossificans progressiva

This is an extremely rare disease of the connective tissue where a mutation of the body's repair mechanism causes fibrous tissue (including muscle, tendon, and ligament) to be ossified when damaged.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

• Calcification or ossification of muscle #17882
• Progressive ossification of skin, skeletal muscle, fascia, tendons or ligaments #18784
• Progressive ossification of skin, skeletal muscle, fascia, tendons or ligaments #23275
• Syndromes with skeletal anomalies as a major feature #23226